An adolescent suffering from Mayer-von Rokitansky-Küster-Hauser syndrome: the importance of an integral multidisciplinary approach
DOI:
https://doi.org/10.18597/rcog.471Keywords:
agenesis vagina, gynecology, pediatricsAbstract
The classical case of an adolescent having had incidental and late diagnosis of Mayer-von Rokitansky-Küster-Hauser syndrome is presented, as are aspects considered fundamental in supporting early diagnosis and treatment of these patients from initial evaluation to detailed description of the surgical procedure. This consisted of a sigmoid neovaginoplasty on three consecutive occasions according to modified Pena procedure. The importance of a multidisciplinary approach is stressed, involving a team qualified in medical, paramedical and psycho-social disciplines, as well as involving the patient and parents in all aspects of the treatment.Author Biographies
Gabriel Barbosa
Mario Varela-Guzmán
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