Ausencia congénita de vagina

William Onatra H., Clara Arteaga, Orlando Pérez

Resumen


Se presentan Jos principales aspectos de la historia, frecuencia, embriología y genética de la ausencia congénita de vagina. Se analizaron 850 historias de la clínica de Endocrinología del Instituto Maternó Infantil durante el período de 1970 a 1988, encontrándose 45 casos (4.1%) de agenesia de vagina, proponiendo Jos autores 4 categorías con los siguientes criterios:

l. Ausencia congénita de vagina con disgenesia gonadal (XX o XY). 4 casos-46XX (8.6%) 12XY (26%).                                                                     II. Ausencia congénita de vagina con gónada normal (síndrome de Rockitansky Kuster Hauser) 19 pacientes (41.4%).                                                       III. Ausencia congénita de vagina con anomalías de fusión de ductus mulerianos (3 pacientes) 3 casos (6.6%).                                                                 IV. Ausencia congénita de vagina con útero y gónada normal (tabiques, longitudinal transverso) 8 pacientes. 8 casos (17.4%).                                

Se propone el siguiente manejo: Grupo I, terapia de suplencia y adopción si la paciente desea. Grupo 11, neovagina y si desea embarazo madre sustituta. Grupo III, insirninación intrauterina. Plastia utrina según el caso. Grupo IV, utilizar la cánula endotraquial para evitar la histerectomía.

 


Palabras clave


Neovagina; plastia vaginal; ausencia vagina

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Referencias


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ISSN Impreso       0034-7434 

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