Ausencia congénita de vagina
DOI:
https://doi.org/10.18597/rcog.887Keywords:
Neovagina, uterine surgery, lack of vaginaAbstract
Se presentan Jos principales aspectos de la historia, frecuencia, embriología y genética de la ausencia congénita de vagina. Se analizaron 850 historias de la clínica de Endocrinología del Instituto Maternó Infantil durante el período de 1970 a 1988, encontrándose 45 casos (4.1%) de agenesia de vagina, proponiendo Jos autores 4 categorías con los siguientes criterios:
l. Ausencia congénita de vagina con disgenesia gonadal (XX o XY). 4 casos-46XX (8.6%) 12XY (26%).
II. Ausencia congénita de vagina con gónada normal (síndrome de Rockitansky Kuster Hauser) 19 pacientes (41.4%).
III. Ausencia congénita de vagina con anomalías de fusión de ductus mulerianos (3 pacientes) 3 casos (6.6%).
IV. Ausencia congénita de vagina con útero y gónada normal (tabiques, longitudinal transverso) 8 pacientes. 8 casos (17.4%).
Se propone el siguiente manejo: Grupo I, terapia de suplencia y adopción si la paciente desea. Grupo 11, neovagina y si desea embarazo madre sustituta. Grupo III, insirninación intrauterina. Plastia utrina según el caso. Grupo IV, utilizar la cánula endotraquial para evitar la histerectomía.
Author Biographies
William Onatra H.
Universidad Nacional de Colombia. Profesor Asistente. Departamento de Obstetricia y Ginecología.
Clara Arteaga
Profesora Asistente. Departamento de Morfología. Seción Genética.
Orlando Pérez
Profesor Asistente. Departamento de Cirugía. Sección Cirugía. Plástica . Universidad Nacional de Colombia. Bogotá.
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